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KMID : 0870420090130040307
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Korean Journal of Hepato-Biliary-Pancreatic Surgery
2009 Volume.13 No. 4 p.307 ~ p.310
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Non-Functioning Somatostatinoma of the Duodenum in Patient with Von Recklinghausen’s Disease
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Kim Kang-Jae
Choi Dong-Wook
Jang Kee-Taek
Kim Woo-Seok
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Abstract
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Somatostatinoma is a rare endocrine tumor that comprises around 1% of all gastroenteropancreatic endocrine neoplasm. The estimated annual incidence is 1 in 40 million. This tumor may be associated with von Recklinghausen’s disease. We present here a rare case of a 51-year-old female patient with a duodenal nonfunctioning somatostatinoma combined with von Recklinghausen’s disease. Whipple’ procedure was performed. The postoperative course was uneventful and the histopathologic findings were consistent with malignant nonfunctioning somatostatinoma with lymph node metastases. The patient is alive, healthy and without tumor recurrence 10 months after surgery.
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KEYWORD
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Neuroendocrine tumors, Somatostatinoma, Von Recklinghausen’s disease
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